D65 | Disseminated intravascular coagulation [defibrination syndrome] | |||||||
Afibrinogenaemia, acquired
Consumption coagulopathy Diffuse or disseminated intravascular coagulation [DIC] Fibrinolytic haemorrhage, acquired Purpura: · fibrinolytic · fulminans |
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Excludes: | that (complicating):
· abortion or ectopic or molar pregnancy · in newborn · pregnancy, childbirth and the puerperium |
D66 | Hereditary factor VIII deficiency | |||||||
Deficiency factor VIII (with functional defect)
Haemophilia: · NOS · A · classical |
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Excludes: | factor VIII deficiency with vascular defect
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D67 | Hereditary factor IX deficiency | |||||||
Christmas disease
Deficiency: · factor IX (with functional defect) · plasma thromboplastin component [PTC] Haemophilia B |
D68 | Other coagulation defects | |||||||
Excludes: | those complicating:
· abortion or ectopic or molar pregnancy · pregnancy, childbirth and the puerperium |
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D68.0 | Von Willebrand's disease | |||||||
Angiohaemophilia
Factor VIII deficiency with vascular defect Vascular haemophilia |
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Excludes: | capillary fragility (hereditary)
factor VIII deficiency: · NOS · with functional defect |
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D68.1 | Hereditary factor XI deficiency | |||||||
Haemophilia C
Plasma thromboplastin antecedent [PTA] deficiency |
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D68.2 | Hereditary deficiency of other clotting factors | |||||||
Congenital afibrinogenaemia
Deficiency: · AC globulin · proaccelerin Deficiency of factor: · I [fibrinogen] · II [prothrombin] · V [labile] · VII [stable] · X [Stuart-Prower] · XII [Hageman] · XIII [fibrin-stabilizing] Dysfibrinogenaemia (congenital) Hypoproconvertinaemia Owren's disease |
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D68.3 | Haemorrhagic disorder due to circulating anticoagulants | |||||||
Haemorrhage during long-term use of anticoagulants
Hyperheparinaemia Increase in: · antithrombin · anti-VIIIa · anti-IXa · anti-Xa · anti-XIa |
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Use additional external cause code (Chapter XX), if desired, to identify any administered anticoagulant. | ||||||||
Excludes: | long-term use of anticoagulants without haemorrhage
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D68.4 | Acquired coagulation factor deficiency | |||||||
Deficiency of coagulation factor due to:
· liver disease · vitamin K deficiency |
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Excludes: | vitamin K deficiency of newborn
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D68.8 | Other specified coagulation defects | |||||||
#D68.80 | Inherited hypercoagulable states,deficiencies of antithrombin III,protein-C,protein-S
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#D68.81 | Acquired hypercoagulable states
Antiphospholipid syndrome
Presence of systemic lupus erythematosus [SLE] inhibitor
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#D68.88 | Other specified coagulation defects | |||||||
D68.9 | Coagulation defect, unspecified |
D69 | Purpura and other haemorrhagic conditions | |||||||
Excludes: | benign hypergammaglobulinaemic purpura
cryoglobulinaemic purpura essential (haemorrhagic) thrombocythaemia purpura fulminans thrombotic thrombocytopenic purpura |
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D69.0 | Allergic purpura | |||||||
Purpura:
· anaphylactoid · Henoch(-Schönlein) · nonthrombocytopenic: · haemorrhagic · idiopathic · vascular Vasculitis, allergic |
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D69.1 | Qualitative platelet defects | |||||||
# | Acquired platelet dysfunction with eosinophilia Bernard-Soulier [giant platelet] syndrome Glanzmann's disease Grey platelet syndrome Thromboasthenia (haemorrhagic)(hereditary) Thrombocytopathy |
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Excludes: | von Willebrand's disease
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D69.2 | Other nonthrombocytopenic purpura | |||||||
Purpura:
· NOS · senile · simplex |
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D69.3 | Idiopathic thrombocytopenic purpura | |||||||
Evans' syndrome
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D69.4 | Other primary thrombocytopenia | |||||||
Excludes: | thrombocytopenia with absent radius
transient neonatal thrombocytopenia Wiskott-Aldrich syndrome |
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D69.5 | Secondary thrombocytopenia | |||||||
Use additional external cause code (Chapter XX), if desired, to identify cause. | ||||||||
D69.6 | Thrombocytopenia, unspecified | |||||||
D69.8 | Other specified haemorrhagic conditions | |||||||
Capillary fragility (hereditary)
Vascular pseudohaemophilia |
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D69.9 | Haemorrhagic condition, unspecified |